Read more. Read clinical updates and the latest insights from Boston Children's specialists. Learn more. Talk to your healthcare provider about getting your child immunized today. In children with Hirschsprung's disease , the intestinal nerve cells ganglion cells don't develop properly. This delays the progression of stool through the intestines.
Abdomino-anal pull-through resection of the rectum.
Hirschsprung Disease - A SAGES Wiki Article
Children can be born with many kinds of malformations. Then they will discuss the best treatment plan for your child. This will often include surgery. Call the Colorectal Center at if you notice any of these issues or if you have any questions or concerns. Find Another Condition or Treatment. Show All. Before Surgery Show.
Clinical outcomes of colo-anal pull-through procedure for complex rectal conditions.
Hirschsprung disease congenital aganglionic megacolon is a developmental disorder of the enteric nervous system, characterized by the absence of ganglion cells in the distal colon resulting in functional obstruction. Whitehouse and Kernohan finally described the pathophysiology in the mid 20th century in a case series of their own which documented the aganglionosis within the distal colon or rectum as the cause of the functional obstruction. In recent years, improvements in surgical technique, and earlier suspicion and diagnosis of the disease, have resulted in an increasing amount of single-stage and minimally invasive procedures.
When a rectal cancer is located at less than 5 cm from the anal verge very low rectal cancer , abdominoperineal resection APR was generally performed 1. However, patients undergoing ISR generally have direct impairment of anal sphincter function because the anal internal sphincter, as a part of the anal sphincter complex, is removed. Moreover, dentate line is also removed resulting in an impairment of sensibility and hence also to more incontinence.